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Pulmonary atresia with intact atrial and ventricular septums, unroofed coronary sinus, and absent aortocoronary arterial connections

Published online by Cambridge University Press:  08 August 2008

Lance K. Erickson ,
Michael D. Puchalski  and
Theodore J. Pysher
Lance K. Erickson*
Affiliation:
Department of Pathology, Primary Children’s Medical Center, Salt Lake City, Utah, United States of America
Michael D. Puchalski
Affiliation:
Department of Cardiology, Primary Children’s Medical Center, Salt Lake City, Utah, United States of America
Theodore J. Pysher
Affiliation:
Department of Pathology, Primary Children’s Medical Center, Salt Lake City, Utah, United States of America
*
Correspondence to: Lance K Erickson, Department of Pathology, Primary Children’s Medical Center, 100 N Mario Capecchi Dr, Salt Lake City, UT 84113, USA. Tel: (801) 662 2150; Fax: (801) 662 2165; E-mail: lance.erickson@imail.org
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Abstract

A stillborn fetus with pulmonary valvar atresia and intact atrial and ventricular septums also had absence of coronary arterial connections from the aorta and an unroofed coronary sinus. A left superior caval vein drained to the dilated coronary sinus. The left coronary artery was anomalously connected to the proximal branch of the right pulmonary artery, and a fistula from the right ventricle supplied the right coronary artery.

Keywords

Congenital heart diseaseanomalous origin of coronary arteriespersistent left superior caval veincoronary arterial fistula
Type
Brief Report
Information
Cardiology in the Young , Volume 18 , Issue 5 , October 2008 , pp. 520 - 522
Copyright
Copyright © Cambridge University Press 2008

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References

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