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Pulmonary atresia with intact ventricular septum associated with aortic coarctation

Published online by Cambridge University Press:  06 August 2009

Arjamand Shauq ,
Gordon Gladman  and
Edmund J Ladusans
Arjamand Shauq*
Affiliation:
Department of Paediatric Cardiology, Alder Hey Children Hospital, Liverpool, United Kingdom
Gordon Gladman
Affiliation:
Department of Paediatric Cardiology, Alder Hey Children Hospital, Liverpool, United Kingdom
Edmund J Ladusans
Affiliation:
Department of Paediatric Cardiology, Alder Hey Children Hospital, Liverpool, United Kingdom
*
Correspondence to: Dr A Shauq, Department of Paediatric Cardiology, Alder Hey Children Hospital, Eaton Rd, Liverpool, L12 2AP, United Kingdom. Tel: 0044-151-2525633; Fax: 0044-151-2525643; E-mail: shauq7@yahoo.com
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Abstract

Pulmonary atresia with intact septum is itself a rare congenital abnormality, albeit known to be associated with other cardiac and non-cardiac anomalies. The combination of right- and left-sided obstructive lesions, however, is extremely rare. We describe a patient having pulmonary atresia with intact septum associated with aortic coarctation, which to the best of our knowledge has been previously described on but one occasion.

Keywords

Congenitalobstructive lesionarterial duct
Type
Brief Report
Information
Cardiology in the Young , Volume 19 , Issue 5 , October 2009 , pp. 522 - 523
Copyright
Copyright © Cambridge University Press 2009

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