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Pulmonary haemodynamics in Fontan physiology after lobectomy in a patient with a single ventricle associated with pulmonary sequestration

Part of: Functionally Univentricular Heart Hypoplastic Left Heart Syndrome (HLHS)

Published online by Cambridge University Press:  30 August 2016

Sayaka Mii ,
Kazushi Yasuda  and
Hiroomi Murayama
Sayaka Mii
Affiliation:
Department of Pediatric Cardiology, Aichi Children’s Health and Medical Center, Aichi, Japan
Kazushi Yasuda*
Affiliation:
Department of Pediatric Cardiology, Aichi Children’s Health and Medical Center, Aichi, Japan
Hiroomi Murayama
Affiliation:
Department of Cardiac Surgery, Aichi Children’s Health and Medical Center, Aichi, Japan
*
Correspondence to: K. Yasuda, MD, Department of Pediatric Cardiology, Aichi Children’s Health and Medical Center, 7-426 Morioka, Obu, Aichi 474-8710, Japan. Tel: +81 562 43 0500; Fax: +81 562 43 0513; E-mail: kazyasuda@vs01.vaio.ne.jp
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Abstract

A 2-year-old girl with a functionally univentricular heart associated with a pulmonary sequestration underwent right lower lobectomy after which increased lung volume with low mean pulmonary artery pressure and pulmonary vascular resistance was documented. A cardiac catheterisation performed after a subsequent total cavopulmonary connection demonstrated favourable Fontan haemodynamics. Lobectomy may have induced compensatory lung growth, contributing to the maintenance of haemodynamics favourable for the long-term success of the Fontan procedure.

Keywords

Compensatory lung growthpulmonary arterial growthpulmonary vascular resistancepulmonary vascular bedtotal cavopulmonary connection
Type
Brief Report
Information
Cardiology in the Young , Volume 27 , Issue 2 , March 2017 , pp. 381 - 384
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Copyright
© Cambridge University Press 2016 

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