Hostname: page-component-cd9895bd7-p9bg8 Total loading time: 0 Render date: 2024-12-28T06:08:16.517Z Has data issue: false hasContentIssue false

Repair of a mixed form of supracardiac total anomalous pulmonary venous connection

Published online by Cambridge University Press:  03 November 2020

Yuki Kawasaki
Affiliation:
Division of Cardiology, Children’s Hospital of Michigan, Department of Paediatrics, Wayne State University School of Medicine, Detroit, MI, USA Division of Paediatric Cardiology, Osaka City General Hospital Paediatric Medical Center, Osaka, Japan
John N. Dentel
Affiliation:
Division of Cardiovascular Surgery, Children’s Hospital of Michigan, Department of Surgery, Wayne State University School of Medicine, Detroit, MI, USA
Henry L. Walters III
Affiliation:
Division of Cardiovascular Surgery, Children’s Hospital of Michigan, Department of Surgery, Wayne State University School of Medicine, Detroit, MI, USA
James M. Galas
Affiliation:
Division of Cardiology, Children’s Hospital of Michigan, Department of Paediatrics, Wayne State University School of Medicine, Detroit, MI, USA
Daisuke Kobayashi*
Affiliation:
Division of Cardiology, Children’s Hospital of Michigan, Department of Paediatrics, Wayne State University School of Medicine, Detroit, MI, USA
*
Author for correspondence: D. Kobayashi, MD, Division of Cardiology, Children’s Hospital of Michigan, 3901 Beaubien Blvd, Detroit, MI 48201-2119, USA. Tel: +1 313 745 5481; Fax: +1 313 993 0894. E-mail: dkobayas@dmc.org

Abstract

Total anomalous pulmonary venous connection is a rare congenital heart defect. We report an infant with a mixed form of supracardiac TAPVC, in whom all pulmonary veins, except the right upper, entered a pulmonary venous confluence that is connected to a vertical vein and drained into the superior vena caval–right atrial junction. Several segmental right upper pulmonary veins entered the superior vena cava, superior to the entry of the vertical vein. Surgical repair consisted of the Warden procedure combined with direct anastomosis of the vertical vein to the left atrium. Separate pulmonary venous drainage pathways decreased the risk of post-operative pulmonary venous obstruction. Our patient had an uneventful post-operative course and encouraging 2-month follow-up echocardiography. Careful follow-up is warranted to detect post-operative complications, including obstruction of the pulmonary venous and cavoatrial anastomoses.

Type
Brief Report
Copyright
© The Author(s), 2020. Published by Cambridge University Press

Access options

Get access to the full version of this content by using one of the access options below. (Log in options will check for institutional or personal access. Content may require purchase if you do not have access.)

References

Franklin, RCG, Béland, MJ, Colan, SD, et al. Nomenclature for congenital and paediatric cardiac disease: the International Paediatric and Congenital Cardiac Code (IPCCC) and the Eleventh Iteration of the International Classification of Diseases (ICD-11). Cardiol Young 2017; 27: 18721938.Google Scholar
Warden, HE, Gustafson, RA, Tarnay, TJ, Neal, WA. An alternative method for repair of partial anomalous pulmonary venous connection to the superior vena cava. Ann Thorac Surg 1984; 38: 601605.CrossRefGoogle ScholarPubMed
DiBardino, DJ, McKenzie, ED, Heinle, JS, Su, JT, Fraser, CD Jr The Warden procedure for partially anomalous pulmonary venous connection to the superior caval vein. Cardiol Young 2004; 14: 6467.CrossRefGoogle ScholarPubMed
Park, CS, Kwak, JG, Lee, C, et al. Partial anomalous pulmonary venous connection to the superior vena cava: the outcome after the Warden procedure. Eur J Cardiothorac Surg 2012; 41: 261265.CrossRefGoogle ScholarPubMed
Craig, JM, Darling, RC, Rothney, WB. Total pulmonary venous drainage into the right side of the heart: report of 17 autopsied cases not associated with other major cardiovascular anomalies. Lab Invest 1957; 6: 4464.Google Scholar
Supplementary material: Image

Kawasaki et al. supplementary material

Kawasaki et al. supplementary material 1

Download Kawasaki et al. supplementary material(Image)
Image 541.9 KB
Supplementary material: Image

Kawasaki et al. supplementary material

Kawasaki et al. supplementary material 2

Download Kawasaki et al. supplementary material(Image)
Image 1.2 MB
Supplementary material: Image

Kawasaki et al. supplementary material

Kawasaki et al. supplementary material 3

Download Kawasaki et al. supplementary material(Image)
Image 5.7 MB