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Right aortic arch with isolation of the left subclavian artery: a rare association with airway obstruction

Published online by Cambridge University Press:  07 November 2016

Putri Yubbu ,
Haifa A. Latiff  and
Abdel Moneim Adam Abbaker
Putri Yubbu*
Affiliation:
Department of Pediatric, Faculty of Medicine and Health Science, University Putra Malaysia, Serdang, Selangor, Malaysia
Haifa A. Latiff
Affiliation:
Department of Paediatric Cardiology, National Health Institute, Kuala Lumpur, Malaysia
Abdel Moneim Adam Abbaker
Affiliation:
Cardiothoracic Surgery Department, National Health Institute, Kuala Lumpur, Malaysia
*
Correspondence to: P. Yubbu, Pediatric Department, Faculty of Medicine and Health Sciences, University Putra Malaysia, 43400 Serdang, Selangor, Malaysia. Tel: +60 13 733 4543; Fax: +603 8948 2507; E-mail: putri7237@gmail.com
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Abstract

We present two interesting cases of isolated left subclavian artery from the pulmonary artery with symptoms of upper airway obstruction. The first patient had tetralogy of Fallot, pulmonary artery sling, bilateral superior caval veins, and left bronchial isomerism, suggesting heterotaxy syndrome. The second patient had a right aortic arch, isolated left subclavian artery, and bilateral arterial ducts. These two cases are interesting because of their rarity and uncommon presentation.

Keywords

Isolated subclavian arterypulmonary artery slingairway obstructionvascular ringleft bronchial isomerism
Type
Brief Report
Information
Cardiology in the Young , Volume 27 , Issue 3 , March 2017 , pp. 613 - 616
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Copyright
© Cambridge University Press 2016 

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