Hostname: page-component-cd9895bd7-8ctnn Total loading time: 0 Render date: 2024-12-28T21:16:03.411Z Has data issue: false hasContentIssue false
  • English
  • Français

Right aortic arch with isolation of the left subclavian artery: a rare association with airway obstruction

Published online by Cambridge University Press:  07 November 2016

Putri Yubbu ,
Haifa A. Latiff  and
Abdel Moneim Adam Abbaker
Putri Yubbu*
Affiliation:
Department of Pediatric, Faculty of Medicine and Health Science, University Putra Malaysia, Serdang, Selangor, Malaysia
Haifa A. Latiff
Affiliation:
Department of Paediatric Cardiology, National Health Institute, Kuala Lumpur, Malaysia
Abdel Moneim Adam Abbaker
Affiliation:
Cardiothoracic Surgery Department, National Health Institute, Kuala Lumpur, Malaysia
*
Correspondence to: P. Yubbu, Pediatric Department, Faculty of Medicine and Health Sciences, University Putra Malaysia, 43400 Serdang, Selangor, Malaysia. Tel: +60 13 733 4543; Fax: +603 8948 2507; E-mail: putri7237@gmail.com
Get access Rights & Permissions [Opens in a new window]

Abstract

We present two interesting cases of isolated left subclavian artery from the pulmonary artery with symptoms of upper airway obstruction. The first patient had tetralogy of Fallot, pulmonary artery sling, bilateral superior caval veins, and left bronchial isomerism, suggesting heterotaxy syndrome. The second patient had a right aortic arch, isolated left subclavian artery, and bilateral arterial ducts. These two cases are interesting because of their rarity and uncommon presentation.

Keywords

Isolated subclavian arterypulmonary artery slingairway obstructionvascular ringleft bronchial isomerism
Type
Brief Report
Information
Cardiology in the Young , Volume 27 , Issue 3 , March 2017 , pp. 613 - 616
Check for updates
Copyright
© Cambridge University Press 2016 

Access options

Get access to the full version of this content by using one of the access options below. (Log in options will check for institutional or personal access. Content may require purchase if you do not have access.)

References

1. Edwards, JE. Anomalies of the derivatives of the arch system. Med Clin North Am 1948; 32: 925–949.Google Scholar
2. Carano, N, Piazza, P, Agnetti, A, et al. Congenital pulmonary steal phenomenon associated with tetralogy of Fallot, right aortic arch, and isolation of the left subclavian artery. Pediatr Cardiol 1997; 18: 57–60.Google Scholar
3. Landing, BH, Dixon, LG. Congenital malformations and genetic disorders of the respiratory tract (larynx, trachea, bronchi, and lungs). Am Rev Respir Dis 1979; 120: 151–185.Google Scholar
4. Bricker, JT, Nihill, MR, McNamara, DG. Tetralogy of Fallot and congenital connection between left subclavian artery and pulmonary artery: possible relationship to a congenital left-hand deformity. Tex Heart Inst J 1984; 11: 84–88.Google Scholar
5. Sade, RM, Rosenthal, A, Fellows, K, et al. Pulmonary artery sling. J Thorac Cardiovasc Surg 1975; 69: 333–346.Google Scholar
6. Miller, SG, Campbell, MJ, Barker, PC, et al. Isolated right subclavian artery arising from the right pulmonary artery via a right-sided ductus arteriosus with associated pulmonary steal phenomenon. Cardiol Young 2012; 22: 216–218.Google Scholar
7. Filler, RM, de Fraga, JC. Tracheomalacia. Semin Thorac Cardiovasc Surg 1994; 6: 211–215.Google ScholarPubMed
8. Gikonyo, BM, Jue, KL, Edwards, JE. Pulmonary vascular ring: report of seven cases and review of literature. Pediatr Cardiol 1989; 10: 81–89.Google Scholar
9. Peyvandi, S, Lupo, PJ, Garbarini, J, et al. 22q11.2 deletions in patients with conotruncal defects: data from 1610 consecutive cases. Pediatr Cardiol 2013; 34: 1687–1694.Google Scholar
10. Van Son, JA, Julsrud, PR, Hagler, DJ, et al. Imaging strategies for vascular rings. Ann Thorac Surg 1994; 57: 604–610.Google Scholar