Hostname: page-component-cd9895bd7-dk4vv Total loading time: 0 Render date: 2024-12-27T07:45:15.591Z Has data issue: false hasContentIssue false
  • English
  • Français

Severely obstructed totally anomalous pulmonary venous return with residual connection to the left atrium

Published online by Cambridge University Press:  18 June 2007

Lik Eng Loh ,
Katherine Brown  and
Jan Marek
Lik Eng Loh
Affiliation:
Cardiothoracic Unit, Great Ormond Street Hospital for Sick Children, London, United Kingdom
Katherine Brown
Affiliation:
Cardiothoracic Unit, Great Ormond Street Hospital for Sick Children, London, United Kingdom
Jan Marek*
Affiliation:
Cardiothoracic Unit, Great Ormond Street Hospital for Sick Children, London, United Kingdom
*
Correspondence to: Dr Jan Marek, MD, PhD, Director of Echocardiography, Consultant Paediatric Cardiologist, Great Ormond Street Hospital for Sick Children, Great Ormond Street, London WC1N 3JH, United Kingdom. Tel: +44 (0)207 405 9200, Ext 8012; Fax: +44 (0)207 813 8262; E-mail: MarekJ@gosh.nhs.uk
Get access Rights & Permissions [Opens in a new window]

Abstract

Totally anomalous pulmonary venous return may present diagnostic difficulty to clinicians, as it often appears similar to severe neonatal pulmonary disease. We describe a neonate who presented with severely obstructed pulmonary venous return, but with a residual venous connection to the left atrium. The unusual anatomy confounded the diagnosis. To our knowledge, this particular permutation has not previously been described. Our experience indicates that echocardiographic interrogation should be repeated in cases where there is no response to conventional therapy, and all individual pulmonary veins should be observed carefully.

Keywords

Echocardiographyextracorporeal membrane oxygenationcongenital heart disease
Type
Brief Report
Information
Cardiology in the Young , Volume 17 , Issue 4 , August 2007 , pp. 441 - 444
Copyright
Copyright © Cambridge University Press 2007

Access options

Get access to the full version of this content by using one of the access options below. (Log in options will check for institutional or personal access. Content may require purchase if you do not have access.)

References

1. Friedman, WF, Silverman, N. Congenital heart disease in infancy and childhood. E.D.P.P. Heart disease: a textbook of cardiovascular medicine, 6th edn. WB Saunders, Philadelphia, 2001.Google Scholar
2. Darling, RC, Rothurney, WB, Craig, JM. Total pulmonary venous drainage into the right side of the heart: report of 17 autopsied cases not associated with other major cardiovascular abnormalities. Lab Invest 1957; 6: 44–64.Google Scholar
3. Delisle, G, Ando, M, Calder, AL, et al. . Total anomalous pulmonary venous connection: report of 93 autopsied cases with emphasis on diagnostic and surgical considerations. Am Heart J 1976; 91: 99–122.CrossRefGoogle ScholarPubMed
4. Imoto, Y, Kado, H, Asou, T, Shiokawa, Y, Tominaga, R, Yasui, H. Mixed type of total anomalous pulmonary venous connection. Ann Thorac Surg 1998; 66: 1394–1397.CrossRefGoogle ScholarPubMed
5. Cayre, RO, Civetta, JD, Rolden, AO, Rousseau, JJ, Knudson, OA, Valdes-Cruz, LM. Mixed total anomalous pulmonary venous connection: case report with bilateral venous collectors. J Am Soc Echocardiogr 2003; 16: 84–87.Google Scholar
6. Kung, GC, Gao, H, Wong, PC, Sklansky, MS, Uzunyan, MY, Wood, JC. Total anomalous pulmonary venous return involving drainage above, below, and to the heart: a mixed bag. J Am Soc Echocardiogr 2004; 17: 1084–1085.Google Scholar
7. Bando, K, Turrentine, MW, Ensing, GJ, et al. . Surgical management of total anomalous pulmonary venous connection: thirty-year trends. Circulation 1996; 94: 1112–1126.Google Scholar
8. Brown, KL, Miles, F, Sullivan, ID, et al. . Outcome in neonates with congenital heart disease referred for respiratory extracorporeal membrane oxygenation. Acta Paediatr 2005; 94: 1280–1284.CrossRefGoogle ScholarPubMed