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Successful implantation of a dual-chamber pacemaker in an ELBW infant for long QT syndrome

Published online by Cambridge University Press:  06 June 2014

Brian McCrossan ,
Yves d’Udekem ,
Andrew Mark Davis  and
Andreas Pflaumer
Brian McCrossan*
Affiliation:
Department of Paediatric Cardiology, Murdoch Children’s Research Institute and University of Melbourne, Royal Children’s Hospital, Melbourne, Australia
Yves d’Udekem
Affiliation:
Department of Paediatric Cardiac Surgery, Royal Children’s Hospital, Melbourne, Australia
Andrew Mark Davis
Affiliation:
Department of Paediatric Cardiology, Murdoch Children’s Research Institute and University of Melbourne, Royal Children’s Hospital, Melbourne, Australia
Andreas Pflaumer
Affiliation:
Department of Paediatric Cardiology, Murdoch Children’s Research Institute and University of Melbourne, Royal Children’s Hospital, Melbourne, Australia
*
Correspondence to: Dr B. McCrossan, Department of Paediatric Cardiology, Royal Children’s Hospital, 50 Flemington Road, Parkville, Melbourne, Victoria 3052, Australia. Tel: +613 9345 5713; Fax: +613 9345 6001; E-mail: brianmccrossan@doctors.org.uk
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Abstract

Long QT syndromes encompass the most prevalent group of ion channelopathies. Long QT syndromes are predominantly familial and predispose the affected individual to ventricular arrhythmias and sudden death. Permanent pacemaker insertion for long QT syndrome is discouraged apart from younger patients exhibiting 2:1 atrioventricular block. However, permanent pacemaker insertion is a relatively common procedure in neonates with atrioventricular block, and dual-chamber permanent pacemaker insertion in low birth weight infants is challenging. We describe the management of long QT syndrome − type 2 − presenting in an extremely preterm neonate including epicardial, dual-chamber permanent pacemaker insertion.

Keywords

Long QT syndromedual-chamber pacemakerlow birth weight
Type
Brief Reports
Information
Cardiology in the Young , Volume 25 , Issue 3 , March 2015 , pp. 600 - 602
Copyright
© Cambridge University Press 2014 

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