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Successful living donor liver transplantation after stent implantation in a patient with Alagille syndrome and severe bilateral pulmonary artery stenosis

Part of: Interventional Cardiology

Published online by Cambridge University Press:  30 August 2018

Kentaro Akagi Open the ORCID record for Kentaro Akagi [Opens in a new window] ,
Toshikatsu Tanaka  and
Shiro Baba
Kentaro Akagi
Affiliation:
Department of Pediatrics, Graduate School of Medicine, Kyoto University Hospital, Kyoto, Japan
Toshikatsu Tanaka
Affiliation:
Department of Pediatric Cardiology, Hyogo Prefectural Kobe Children’s Hospital, Kobe, Japan
Shiro Baba*
Affiliation:
Department of Pediatrics, Graduate School of Medicine, Kyoto University Hospital, Kyoto, Japan
*
Author for correspondence: S. Baba, MD, PhD, Department of Pediatrics, Graduate School of Medicine, Kyoto University Hospital, 54 Kawahara-cho, Shogoin, Sakyo-ku, Kyoto 606-8507, Japan. Tel: +81 75 751 3295 (3291); Fax: +81 75 752 2361; E-mail: shibaba@kuhp.kyoto-u.ac.jp
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Abstract

Severe pulmonary hypertension is a contraindication for liver transplantation owing to high mortality. However, decision-making regarding the treatment approach for patients with bilateral peripheral pulmonary artery stenosis, typically complicated by elevated main pulmonary artery and right ventricle pressures, can be challenging. Here, we report successful living donor liver transplantation after bilateral pulmonary artery stent implantation in a patient with Alagille syndrome, severe bilateral peripheral pulmonary artery stenosis, and extremely high main pulmonary artery and right ventricle pressures.

Keywords

Peripheral pulmonary artery stenosisliver transplantationstent implantation
Type
Brief Report
Information
Cardiology in the Young , Volume 28 , Issue 12 , December 2018 , pp. 1465 - 1467
Copyright
© Cambridge University Press 2018 

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