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Surgical revisions and mechanical support of the failing Fontan

Published online by Cambridge University Press:  09 January 2014

Stephanie Fuller
Stephanie Fuller*
Affiliation:
Perelman School of Medicine, The Cardiac Center, Division of Cardiothoracic Surgery, The Children's Hospital of Philadelphia, University of Pennsylvania, Philadelphia, Pennsylvania, United States of America
*
Correspondence to: S. Fuller, Perelman School of Medicine, The Cardiac Center, Division of Cardiothoracic Surgery, The Children's Hospital of Philadelphia, University of Pennsylvania, Philadelphia, PA 19104, United States of America. Tel: 215-590-2708; Fax: 215-590-2715; E-mail: fullers@email.chop.edu
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Abstract

Despite its many anatomic modifications, Fontan failure remains prevalent in adult patients living with single-ventricle physiology. Although the Fontan operation has created a generation of survivors of complex single-ventricle disease, recognition of the limitation of this circulation is increasing. Most commonly, survivors suffer from ventricular dysfunction, protein-losing enteropathy, plastic bronchitis and arrhythmias. Although several medical therapies exist to palliate these long-term complications, surgical treatments are becoming increasingly useful, including the introduction of mechanical devices and cardiac transplantation. Currently, there are a variety of options available for mechanical support of the failing Fontan. Further developments in mechanical support technology will be required to tailor-make specific devices for this unique population. Owing to the fact that availability of donor hearts for transplantation is limited, mechanical support will play an increasingly important role in the management of complications of the Fontan circulation.

Keywords

Fontan, congenital heart diseaseventricular assist deviceheart transplantationsingle ventricle
Type
Original Article
Information
Cardiology in the Young , Volume 23 , Issue 6: HeartWeek 2013 , December 2013 , pp. 847 - 851
Copyright
Copyright © Cambridge University Press 2013 

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