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Targeted neonatal echocardiography-guided therapy pre-embolisation for congenital hepatic vascular malformation: inhaled nitric oxide to prevent paradoxical embolisation to the systemic circulation

Published online by Cambridge University Press:  16 November 2020

Adrianne R. Bischoff
Affiliation:
Department of Paediatrics, University of Iowa, Iowa City, IA, USA
Patrick J. McNamara
Affiliation:
Department of Paediatrics, University of Iowa, Iowa City, IA, USA Department of Internal Medicine, University of Iowa, Iowa City, IA, USA
Regan E. Giesinger*
Affiliation:
Department of Paediatrics, University of Iowa, Iowa City, IA, USA
*
Author for correspondence: R. E. Giesinger, MD, BScH, FRCPC, University of Iowa, 200 Hawkins Dr, Iowa City, IA 52242, USA. Tel: +1 319 467 7435; Fax: +1 319 356-4685.E-mail: regan-giesinger@uiowa.edu

Abstract

Arteriovenous malformations may present with significant haemodynamic compromise in the neonatal period, typically with high output cardiac failure that may be accompanied by hypoxia and right ventricular dysfunction. Targeted neonatal echocardiography performed by trained neonatologists provides an enhanced physiology-based approach that can guide treatment and minimise complications. We present a case of a large hepatic vascular malformation whose therapy was guided by targeted neonatal echocardiography to prevent paradoxical embolisation of procedural glue to the systemic circulation.

Type
Brief Report
Copyright
© The Author(s), 2020. Published by Cambridge University Press

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