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Three-dimensional echocardiographic evaluation of Ebstein’s anomaly of the tricuspid valve in a patient with hypoplastic left heart syndrome

Part of: Echocardiography Hypoplastic Left Heart Syndrome (HLHS)

Published online by Cambridge University Press:  22 April 2018

Courtney Cassidy Open the ORCID record for Courtney Cassidy [Opens in a new window] ,
Max B. Mitchell  and
Pei-Ni Jone
Courtney Cassidy*
Affiliation:
Children’s Hospital Colorado, Aurora, CO, USA
Max B. Mitchell
Affiliation:
Cardiovascular Surgery, Children’s Hospital Colorado, University of Colorado School of Medicine, Aurora, CO, USA
Pei-Ni Jone
Affiliation:
Pediatric Cardiology, Children’s Hospital Colorado, University of Colorado School of Medicine, Aurora, CO, USA
*
Author for correspondence: C. Cassidy, RDCS, Children’s Hospital Colorado, 13123 East 16th Avenue, Aurora, CO 80045, USA. Tel: 720 777 2949; Fax: 1 720 777 7174; E-mail: courtney.cassidy@childrenscolorado.org
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Abstract

We report three-dimensional imaging of a rare finding of Ebstein’s anomaly of the tricuspid valve in a patient with hypoplastic left heart syndrome, which has been previously reported only by two-dimensional echocardiography. A fetal echocardiogram was performed at 19 weeks that showed a moderately hypoplastic left ventricle, severely hypoplastic mitral valve, a severely hypoplastic aortic valve, and a dysplastic tricuspid valve. Post Caesarean delivery at 40 weeks of gestation, a transthoracic echocardiogram confirmed the findings seen on the fetal echocardiogram. A three-dimensional echocardiogram was then performed, which demonstrated an Ebstein tricuspid valve with apical displacement of the septal leaflet, chordal attachments of the valve to the right ventricular outflow tract, and moderate tricuspid regurgitation. The patient underwent a successful heart transplantation.

Keywords

Ebstein’s anomalyhypoplastic left heart syndrome3D echocardiographytricuspid valve regurgitationechocardiography and scans
Type
Brief Report
Information
Cardiology in the Young , Volume 28 , Issue 6 , June 2018 , pp. 885 - 887
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Copyright
© Cambridge University Press 2018 

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References

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