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Unusual sudden cardiac death from an anomalous left coronary artery from the right sinus of Valsalva

Published online by Cambridge University Press:  23 July 2013

Ram N. Bishnoi ,
Kristen N. McMillan  and
William R. Thompson
Ram N. Bishnoi*
Affiliation:
Department of Pediatric Cardiology, Johns Hopkins School of Medicine, Baltimore, Maryland, United States of America
Kristen N. McMillan
Affiliation:
Department of Pediatrics and Department of Anesthesiology and Critical Care Medicine, Johns Hopkins School of Medicine, Baltimore, Maryland, United States of America
William R. Thompson
Affiliation:
Department of Pediatric Cardiology, Johns Hopkins School of Medicine, Baltimore, Maryland, United States of America
*
Correspondence to: R. N. Bishnoi, Department of Pediatric Cardiology, Johns Hopkins School of Medicine, 1800 Orleans Street, Bloomberg Children's Center M2328, Baltimore, MD 21287, United States of America. Tel: +267 275 4560; Fax: +410 955 0897; E-mail: rbishno1@jhmi.edu
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Abstract

A left coronary artery arising from the right sinus of Valsalva is a rare congenital coronary anomaly. We report a case of a 5-year-old boy with an anomalous left coronary artery from the right sinus of Valsalva whose presenting sign was cardiac arrest. There is no reported instance of a child <9 years of age without other congenital cardiac defects having died suddenly with this coronary anomaly. The transthoracic echocardiogram demonstrated normal origins of the coronary arteries, but on autopsy, an anomalous origin of the left main coronary artery from the right sinus of Valsalva was found.

Keywords

Anomalous aortic origin of a coronary artery (AAOCA)anomalous origin of the left main coronary artery from the right sinus of Valsalvasudden cardiac death
Type
Brief Reports
Information
Cardiology in the Young , Volume 24 , Issue 4 , August 2014 , pp. 732 - 734
Copyright
Copyright © Cambridge University Press 2013 

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